MCCC1 Polyclonal Antibody
| 规格： | / 20μL / 60μL / 120μL / 200μL |
| 价格： | / ￥420 / ￥1010 / ￥1640 / ￥2365 |
货号：E-AB-52772
宿主: Rabbit
反应性: H,M
应用: WB,IHC
Overview
| Synonyms | 3-methylcrotonyl-CoA carboxylase 1,3-methylcrotonyl-CoA carboxylase biotin-containing subunit,3-methylcrotonyl-CoA carboxylase, alpha,3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha,DKFZp686B20267,FLJ25545,MCC-B,MCCA,MCCase subunit alpha,methylcrotonoyl-CoA carboxylase 1 (alpha),methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial,methylcrotonoyl-Coenzyme A carboxylase 1 (alpha),MCCC1抗体 |
| Swissprot | Q96RQ3 |
| Source | Rabbit |
| Reactivity | Human, Mouse |
| Immunogen | Fusion protein of human MCCC1 |
| Application | WB(Detection kit: E-IR-R304),IHC(Detection kit: E-IR-R213) |
| Recommended dilution | WB,,1:500-1:2000;IHC,,1:40-1:200; |
| Concentration | 0.78mg/mL |
| Clonality | Polyclonal |
Properties
| Cellular localization | Mitochondrion matrix. |
| Isotype | IgG |
| Purification | Affinity purification |
| Conjugation | Unconjugated |
| Storage instructions | Store at -20℃. Avoid freeze / thaw cycles. |
| Storage buffer | PBS with 0.05% NaN3 and 40% Glycerol,pH7.4 |
| Background | This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. |
