OTC Polyclonal Antibody
| 规格： | / 20μL / 60μL / 120μL / 200μL |
| 价格： | / ￥420 / ￥1010 / ￥1640 / ￥2365 |
货号：E-AB-11461
宿主: Rabbit
反应性: H,M,R
应用: WB,IHC
Overview
| Synonyms | EC 2.1.3.3,MGC129967,MGC129968,MGC138856,OCTD,Ornithine carbamoyltransferase mitochondrial,Ornithine carbamoyltransferase,mitochondrial,Ornithine transcarbamylase,Otc,OTC,OTCase,OTC抗体 |
| Swissprot | P00480 |
| Source | Rabbit |
| Reactivity | Human,Mouse,Rat |
| Immunogen | Recombinant protein of human OTC |
| Application | WB(Detection kit: E-IR-R304),IHC(Detection kit: E-IR-R213) |
| Recommended dilution | WB,,1:500-1:2000;IHC,,1:50-1:200; |
| Concentration | 0.6 mg/mL |
| Clonality | Polyclonal |
Properties
| Cellular localization | Mitochondrion matrix. |
| Tissue specificity | Mainly expressed in liver and intestinal mucosa. |
| Isotype | IgG |
| Purification | Affinity purification |
| Conjugation | Unconjugated |
| Storage instructions | Store at -20℃. Avoid freeze / thaw cycles. |
| Storage buffer | PBS with 0.05% sodium azide, 50% glycerol, PH7.3 |
| Background | This nuclear gene encodes a mitochondrial matrix enzyme.Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia.Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. |
